Elevated ethylmalonic acid can be a result of Nrf2 activation
Nrf2 Cystine Persulfides xCT SLC7A11 SQOR
Coenzyme Q10 upregulates SQOR and downregulates CBS, CSE
Transsulfuration CBS CSE SQOR CQ10
Supercomplexes in ETC
ETC Respirosome RET GPD2 CHDH ETFDH SQOR PRODH DHODH